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Case Reports
Administration of Sugammadex Intraoperatively in a Patient With a Congenital Myasthenic Syndrome: A Case Report.
- Adlai L Pappy, Carie Ann F Sirmon, and Shivani G Mukkamala.
- From the Department of Anesthesiology and Pain Medicine, Brigham and Women's Hospital, Boston, Massachusetts.
- A A Pract. 2021 Mar 24; 15 (3): e01437.
AbstractCongenital myasthenic syndromes are a group of genetic neuromuscular disorders caused by mutations that impair synaptic transmission at the neuromuscular junction. Developing an anesthetic plan for patients with this diagnosis is difficult, as they are at risk for prolonged neuromuscular blockade. Sugammadex is an alternative to neostigmine for neuromuscular blockade reversal that does not produce muscarinic side effects, yet there is a little literature assessing sugammadex in congenital myasthenic syndromes. We present the case of a 6-year-old boy with a congenital myasthenic syndrome who received sugammadex without complication. This case provides support for clinicians to consider sugammadex in these patients.Copyright © 2021 International Anesthesia Research Society.
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