• Wei Shyan Siow and Wan-Ling Alyssa Chiew.
• Changi General Hospital, Singhealth. 2 Simei Street 3, 529889, Singapore, Singapore. swshyan@gmail.com.
• BMC Anesthesiol. 2021 Feb 18; 21 (1): 57.

BackgroundParamyotonia congenita is a rare autosomal dominant myopathy which presents with periodic weakness due to cold and exercise. It is caused by mutations of the SCN4 gene which encodes the sodium channel in skeletal muscles.Case PresentationWe report a full term obstetric patient with both paramyotonia congenita and terminal filum lipoma who presents for induction of labour followed by an emergency caesarean section performed under epidural anesthesia. Her recovery is subsequently complicated by a 3-day history of postpartum paraparesis attributed to hypokalemic periodic paralysis.ConclusionWe describe the perioperative anesthesia considerations and challenges in this case with a review of the current literature. This case report highlights the importance of early proactive and collaborative multidisciplinary approach, maintaining normal temperature and electrolytes with a heightened vigilance for muscle-related perioperative complications.

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