• Soufiane Ghailane, Sandra Fauquier, Sébastien Lepreux, and Jean-Charles Le Huec.
• Department of Spinal Surgery Unit 2, Bordeaux University Hospital, Université de Bordeaux, C.H.U Tripode Pellegrin, Place Amélie Raba Léon, 33076, Bordeaux, France.
• Eur Spine J. 2019 Jun 1; 28 (6): 1448-1452.

IntroductionWe report a rare and aggressive case of malignant triton tumor (MTT) at the thoracolumbar junction with foraminal extension mistreated as schwannoma.Materials And MethodsA 70-year-old man with a 2-year history of lower back pain and left L4 radiculopathy with no history of neurofibromatosis.ResultsPre-operative MRI suggested a typical schwannoma. Upon complete marginal resection, histological findings revealed a MTT. The patient presented with a local and regional recurrence and died 10 months after surgery. MTTs are a subgroup of malignant peripheral nerve sheath tumors, which develop from Schwann cells of peripheral nerves or within existing neurofibromas, and display rhabdomyoblastic differentiation.ConclusionBased on the Grand Round case and relevant literature, we present a case of a highly aggressive and fast-growing tumor with a very high local and distant recurrence. There is no consensus treatment plan available and patients usually die shortly after diagnosis.

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