Journal of neuromuscular diseases
The most recent articles from:
J Neuromuscul Dis
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Randomized Controlled Trial
Home-Based Monitoring of Pulmonary Function in Patients with Duchenne Muscular Dystroph.
Loss of pulmonary function is a main cause of early morbidity and mortality in patients with Duchenne muscular dystrophy (DMD). Standard of care guidelines recommend regular assessment of pulmonary function by hospital-based spirometry to detect onset and monitor progression of pulmonary function decline. ⋯ This study demonstrates that home-based monitoring of pulmonary function in adolescent patients with DMD using a HHD is feasible, provides reliable data compared to hospital-based spirometry and is therefore suitable for use in clinical practice and for clinical trials.