Congenital heart disease
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Congenital heart disease · Jan 2010
Adults with Down syndrome: safety and long-term outcome of cardiac operation.
As limited data exist, we sought to review the safety and outcome of cardiac surgery in the adult Down syndrome population. ⋯ At an experienced center, adult patients with Down syndrome can undergo cardiac surgery with a low risk of mortality and acceptable morbidity. Atrial arrhythmias and pulmonary infections are common postoperatively.
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Congenital heart disease · Jan 2010
Review Case ReportsSingle coronary artery with right ventricular fistula: case report and literature review.
We report a rare case of a 6-year-old boy who was diagnosed with coronary artery fistulae communicating with the right ventricle and a left single coronary artery. Preoperative angiography showed a dilated and tortuous single coronary artery draining into the right ventricle. ⋯ His clinical course was uneventful. In this report, we summarize cases of coronary artery fistula with single coronary artery that have been reported in the literature as well as our case.
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Congenital heart disease · Jan 2010
Case ReportsHypoplastic right lung associated with right pulmonary vein stenosis and systemic collateral.
We present a case of a 6-month-old girl diagnosed as unilateral pulmonary vein stenosis (right inferior pulmonary vein) with dextroposition of the heart, hypoplastic right lung, hypoplastic right pulmonary artery, collateral from the descending aorta supplied right lower lung, connection between collateral and right pulmonary artery with retrograde flow from right pulmonary artery into main pulmonary artery, and right superior and middle pulmonary vein agenesis. A combined modality of imaging including chest film, echocardiography, multidetector computerized tomography, and the cardiac catheterization nicely demonstrated all of the unique and rare congenital abnormalities.
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Congenital heart disease · Jan 2010
Rehabilitation program in adult congenital heart disease patients with pulmonary hypertension.
It is commonly believed that physical activity may have a negative impact on pulmonary hypertension patients. The object of this study is to determine the tolerability of a directed exercise program in congenital heart disease patients with pulmonary hypertension. ⋯ Cardiopulmonary rehabilitation appears to be a safe intervention in patients with congenital heart disease and pulmonary hypertension.
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Congenital heart disease · Jan 2010
Multicenter StudyThree-stage palliation of hypoplastic left heart syndrome in the University HealthSystem Consortium.
The objective of this study was to describe current management and short-term outcomes for patients with hypoplastic left heart syndrome representative of nationwide experience. Additionally, this study identifies risk factors associated with mortality in patients undergoing staged surgical palliation. ⋯ First-stage palliative mortality for hypoplastic left heart syndrome fell dramatically over the past decade, while that for second- and third-stage procedures remained stable. The cumulative operative mortality for three-staged repair of hypoplastic left heart syndrome was 39% over the decade, but fell to 24% for procedures in 2007.