World journal for pediatric & congenital heart surgery
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World J Pediatr Congenit Heart Surg · Apr 2015
Review Biography Historical ArticleJaroslav Stark, MD, FRCS, FACS, FACC--celebrating an icon of pediatric cardiac surgery at age 80 years.
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World J Pediatr Congenit Heart Surg · Apr 2015
Case ReportsLeft coronary artery stenosis causing left ventricular dysfunction in two children with supravalvular aortic stenosis.
Congenital supravalvar aortic stenosis (SVAS) is an arteriopathy associated with Williams-Beuren syndrome (WBS) and other isolated elastin gene deletions. Cardiovascular manifestations associated with WBS are characterized by obstructive arterial lesions such as SVAS and pulmonary artery stenosis in addition to bicuspid aortic valve and mitral valve prolapse. However, coronary artery ostial stenosis may be associated with SVAS, and it increases the risk of sudden death and may complicate surgical management. In this report, we present our experience with two patients having SVAS and left coronary artery ostial stenosis with associated left ventricular dysfunction.
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World J Pediatr Congenit Heart Surg · Apr 2015
ReviewThe role of home monitoring in interstage management of infants following the Norwood procedure.
Although outcomes for infants with complex single ventricle heart defects have steadily improved in recent decades, there is still a significant risk for mortality and morbidity during the interstage period between stage 1 Norwood hospitalization discharge and stage 2 palliation. Home monitoring programs, which involve parental surveillance of daily weight and oxygen saturations during the interstage period, have been shown to significantly improve survival rates. This article describes the potential risk factors or causes of interstage mortality and reviews the role of home monitoring in early detection and potential prevention of adverse outcomes.
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World J Pediatr Congenit Heart Surg · Apr 2015
Case ReportsPostpartum pulmonary embolism in a patient with Fontan circulation.
Pregnancy is typically not recommended in patients with Fontan circulation. Although patients are well aware of the risks for the mother and fetus, an increasing number opt to become pregnant. ⋯ Postpartum thromboembolism is a known complication, but its prevalence and management are not clearly defined. We present a case of massive pulmonary embolism two weeks postpartum in a patient with double inlet left ventricle palliated with lateral tunnel Fontan.