Revista de la Facultad de Ciencias Médicas
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Rev Fac Cien Med Univ Nac Cordoba · Jun 2019
Case ReportsBilateral single sesion whole lung lavage under venous-venous ECMO in a case of severe pulmonary alveolar proteinosis: five years follow up.
Introduction: Pulmonary alveolar proteinosis (PAP) is a rare disease caused by accumulation of proteinaceous material in the alveolar spaces. The most common mechanism implied is the development of antibodies directed to granulocyte macrophage colony stimulating factor (GM-CSF). which inhibits activation of alveolar macrophage, thereby causing accumulation of surfactant. Standard treatment is considered to be whole lung lavage (WLL).