Pediatric transplantation
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Pediatric transplantation · Feb 2005
Case ReportsDevelopment of hepatopulmonary syndrome and portopulmonary hypertension in a paediatric liver transplant patient.
Hepatopulmonary syndrome (HPS) and portopulmonary hypertension (PPH) are pulmonary vascular disorders which occur in patients with severe liver disease and/or portal hypertension. Although these syndromes are frequently diagnosed in patients undergoing assessment for liver transplantation, they seldom occur in the same patient. ⋯ HPS and PPH may coexist however they may show differing responses to liver transplantation with progression of PPH despite the resolution of HPS.