The Tohoku journal of experimental medicine
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Tohoku J. Exp. Med. · Feb 2005
Review Case ReportsGorham disease of the spine: a case report and treatment strategies for this enigmatic bone disease.
Gorham disease is an extremely rare condition of unknown etiology characterized by progressive osteolysis. Only 28 cases of its spinal involvement have been reported, and some of those cases showed kyphosis, kyphoscoliosis, subluxation or dislocation. ⋯ In situ posterior fusion with a hook and rod system and iliac bone grafts were performed, but after surgery, he had complete paraplegia and its cause was uncertain. Based on the unfortunate consequence of the present case and the review of the literature, we propose the treatment strategies for spinal Gorham disease.