Deutsche medizinische Wochenschrift
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Dtsch. Med. Wochenschr. · Dec 2012
Review Comparative Study[Characteristics and management of idiopathic pulmonary fibrosis: INSIGHTS-IPF registry].
Idiopathic pulmonary fibrosis (IPF), a manifestation of chronic progressive fibrosing interstitial pneumonia, is with a prevalence of 2-29 cases per 100,000 individuals a rare disease. Current treatment options are limited, and the mean survival time of the newly diagnosed (mostly elderly) patients is only about 2-3 years. ⋯ It is planned to document 500 patients in 30 centers. The registry will contribute to the optimization of the management of IPF patients in the long term.