Anadolu kardiyoloji dergisi : AKD = the Anatolian journal of cardiology
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Anadolu Kardiyol Derg · Aug 2010
Review[Other causes of pulmonary arterial hypertension: pulmonary veno-occlusive disease, pulmonary capillary hemangiomatosis, porto-pulmonary hypertension, HIV- associated pulmonary arterial hypertension].
Idiopathic pulmonary arterial hypertension (PAH) is included in Group 1 of PAH classification, while pulmonary veno-occlusive disease (PVOD), pulmonary capillary hemangiomatosis (PCH), portopulmonary hypertension (PoPH) and HIV-associated PAH constitute the subgroups of Group I PAH disorders. PVOD has similar clinical presentation, hemodynamic characteristics and genetic background with PAH although main pathology is in venules and definite diagnosis is done by biopsy although not recommended due to high risk of bleeding. ⋯ PoPH is defined as PAH due to primary chronic liver disease associated with intrapulmonary vascular dilatations and hypoxia. HIV associated PAH is a rare complication of HIV-infection, and it is seen especially in HIV-infected patients with intravenous drug abuse.
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Anadolu Kardiyol Derg · Aug 2010
Review[Pulmonary vasoreactivity testing in diagnosis and prognosis of pulmonary hypertension].
Right heart catheterization (RHC) is required for confirmation of the diagnosis of pulmonary hypertension (PH) and to asses the prognosis and etiology. Pulmonary vasoreactivity testing (PVT) is one of the most crucial parts of RHC especially in the suitable patient subsets of pulmonary arterial hypertension (PAH) defined by the most recent guidelines. PVT has substantial importance in defining the most appropriate treatment modality. The aim of this review is to provide a comprehensive review of the literature about PVT and the agents used in PVT, to emphasize the importance of this procedure when done with correct indications with a correct technique and to contribute in the accurate management of PH patients.
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Pulmonary hypertension is a serious disease with a poor prognosis. The diagnosis and assessment of pulmonary hypertension is evolving rapidly with changes in the definition of the disease, diagnostic techniques and follow-up assessment. Different conditions associated with pulmonary hypertension and new diagnostic techniques have led to a need for a systematic diagnostic approach. This review article presents an update on alterations in the diagnostic algorithm.